Langerhan′s cell histiocytosis: A single institutional experience

<b>Background:</b> Langerhans cell histiocytosis (LCH) is a disease that primarily affects bone but can be associated with a clinical spectrum that ranges from a solitary bone lesion with a favorable natural history to a multisystem, life-threatening disease process. <b>Aim:</b&...

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Bibliographic Details
Main Authors: Singh Tejinder, Satheesh C, Appaji L, Aruna Kumari B, Mamatha H, Giri G, Rao Clementina
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd. 2010-01-01
Series:Indian Journal of Medical and Paediatric Oncology
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Online Access:http://www.ijmpo.org/article.asp?issn=0971-5851;year=2010;volume=31;issue=2;spage=51;epage=53;aulast=Singh
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Summary:<b>Background:</b> Langerhans cell histiocytosis (LCH) is a disease that primarily affects bone but can be associated with a clinical spectrum that ranges from a solitary bone lesion with a favorable natural history to a multisystem, life-threatening disease process. <b>Aim:</b> We analyzed our single institutional experience of managing children with LCH. <b>Settings and Design:</b> A total of 40 children of LCH, managed in tertiary cancer center in South India in the period from 2001 to 2005, were evaluated retrospectively. <b>Materials and Methods:</b> Clinicopathological features, laboratory findings, treatment modalities and long-term outcome were analyzed. <b>Results:</b> Children were aged between 2 months and 12 years, with a mean of 3 years. Majority of the children were below 5 years of age. Group B constituted a bulk of children. Disseminated cases were less (five patients). Liver function dysfunction was seen in four (10&#x0025;) children. Pulmonary interstitial infiltrates were seen in two (5&#x0025;) cases. Diabetes insipidus manifested in three patients. There was one death. <b>Conclusion:</b> A better understanding of the etiology and pathogenesis of LCH will result in more directed and efficacious treatment regimens.
ISSN:0971-5851
0975-2129