Terapia con inhibidores de la vía m-TOR en recién nacidos con hiperinsulinismo congénito resistente a diásóxido y octreotida
Resumen: El hiperinsulinismo congénito (HIC) es una enfermedad desafiante y grave en niños, caracterizada por el compromiso difuso del páncreas. Su tratamiento se basa en terapia crónica con diazóxido y/o octreotida, seguida de pancreatectomía parcial, que a menudo no es resolutiva.Se ha descrito pr...
Saved in:
| Main Author: | Patricio Astudillo, MD, MSc |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2025-03-01
|
| Series: | Revista Médica Clínica Las Condes |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S071686402500032X |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
Similar Items
-
Identification of an ABCC8 variant in a kindred with transient diazoxide responsive hyperinsulinism
by: Ryan L Smith, et al.
Published: (2025-07-01) -
Congenital hyperinsulinism in the Ukraine: a 10-year national study
by: Evgenia Globa, et al.
Published: (2024-12-01) -
Congenital hyperinsulinism associated with Hirschsprung’s disease—a report of an extremely rare case
by: Takeshi Shono, et al.
Published: (2020-01-01) -
Clinical and epidemiological profile of congenital hyperinsulinism in Brazil
by: Raphael D. Liberatore Junior, et al.
Published: (2025-04-01) -
[68Ga] labelled Exendin for radioguided surgery of intrapancreatic insulin producing lesions in patients with congenital hyperinsulinism
by: Peter Kühnen, et al.
Published: (2025-08-01)