Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis

A patient with pulmonary lymphangioleiomyomatosis was diagnosed more than 22 years after the onset of symptoms by a thoracoscopic lung biopsy, after a high resolution computerized tomogram of the chest was highly suggestive of the disease. After nearly 30 years since the onset of her symptoms, the p...

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Main Authors: John K Reid, Henrike Rees, Donald Cockcroft
Format: Article
Language:English
Published: Wiley 2002-01-01
Series:Canadian Respiratory Journal
Online Access:http://dx.doi.org/10.1155/2002/958921
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author John K Reid
Henrike Rees
Donald Cockcroft
author_facet John K Reid
Henrike Rees
Donald Cockcroft
author_sort John K Reid
collection DOAJ
description A patient with pulmonary lymphangioleiomyomatosis was diagnosed more than 22 years after the onset of symptoms by a thoracoscopic lung biopsy, after a high resolution computerized tomogram of the chest was highly suggestive of the disease. After nearly 30 years since the onset of her symptoms, the patient leads a relatively normal life with only mildly abnormal lung function and has minimal reduction in her exercise tolerance. There have been few reports of patients surviving for such a long time after the onset of this disease; the literature suggests that most patients die within 15 years of symptom onset.
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series Canadian Respiratory Journal
spelling doaj-art-2ccf170f444842bfa00a2605aaad0d652025-08-20T03:55:12ZengWileyCanadian Respiratory Journal1198-22412002-01-019534234610.1155/2002/958921Long-Term Survival in a Patient with Pulmonary LymphangioleiomyomatosisJohn K Reid0Henrike Rees1Donald Cockcroft2Division of Respiratory Medicine, Department of Medicine, Royal University Hospital, University of Saskatchewan, CanadaDepartment of Pathology, Saskatoon City Hospital, Saskatoon, Saskatchewan, CanadaDivision of Respiratory Medicine, Department of Medicine, Royal University Hospital, University of Saskatchewan, CanadaA patient with pulmonary lymphangioleiomyomatosis was diagnosed more than 22 years after the onset of symptoms by a thoracoscopic lung biopsy, after a high resolution computerized tomogram of the chest was highly suggestive of the disease. After nearly 30 years since the onset of her symptoms, the patient leads a relatively normal life with only mildly abnormal lung function and has minimal reduction in her exercise tolerance. There have been few reports of patients surviving for such a long time after the onset of this disease; the literature suggests that most patients die within 15 years of symptom onset.http://dx.doi.org/10.1155/2002/958921
spellingShingle John K Reid
Henrike Rees
Donald Cockcroft
Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis
Canadian Respiratory Journal
title Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis
title_full Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis
title_fullStr Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis
title_full_unstemmed Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis
title_short Long-Term Survival in a Patient with Pulmonary Lymphangioleiomyomatosis
title_sort long term survival in a patient with pulmonary lymphangioleiomyomatosis
url http://dx.doi.org/10.1155/2002/958921
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AT henrikerees longtermsurvivalinapatientwithpulmonarylymphangioleiomyomatosis
AT donaldcockcroft longtermsurvivalinapatientwithpulmonarylymphangioleiomyomatosis