Sporadic inclusion body myositis in the rheumatology clinic

Sporadic inclusion body myositis (sIBM) is a progressive and insidious skeletal muscle disorder characterized classically by the quadriceps, wrist, and finger flexor weakness. The main irreversible complications of sIBM are dysphagia and walking difficulties. The disease affects more men than women,...

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Main Authors: Fernando Henrique Carlos de Souza, Gustavo Luiz Behrens Pinto, Jean Marcos de Souza, Pablo Arturo Olivo Pallo, Leonardo Santos Hoff, Samuel Katsuyuki Shinjo
Format: Article
Language:English
Published: SAGE Publishing 2020-01-01
Series:Indian Journal of Rheumatology
Subjects:
Online Access:http://www.indianjrheumatol.com/article.asp?issn=0973-3698;year=2020;volume=15;issue=6;spage=145;epage=152;aulast=de
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author Fernando Henrique Carlos de Souza
Gustavo Luiz Behrens Pinto
Jean Marcos de Souza
Pablo Arturo Olivo Pallo
Leonardo Santos Hoff
Samuel Katsuyuki Shinjo
author_facet Fernando Henrique Carlos de Souza
Gustavo Luiz Behrens Pinto
Jean Marcos de Souza
Pablo Arturo Olivo Pallo
Leonardo Santos Hoff
Samuel Katsuyuki Shinjo
author_sort Fernando Henrique Carlos de Souza
collection DOAJ
description Sporadic inclusion body myositis (sIBM) is a progressive and insidious skeletal muscle disorder characterized classically by the quadriceps, wrist, and finger flexor weakness. The main irreversible complications of sIBM are dysphagia and walking difficulties. The disease affects more men than women, and the symptom onset mainly occurs between 50 and 70 years of age. Due to its slow progression, sIBM diagnosis is frequently delayed and therefore misdiagnosed as other muscle diseases. sIBM remains refractory to treatment (e.g., glucocorticoid, and immunosuppressive/immunomodulatory/immunobiological drugs). Although there have been no robust clinical trials, training exercise/physiotherapy should be prescribed regularly in sIBM patients.
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series Indian Journal of Rheumatology
spelling doaj-art-2bc9d93215214e3fa1c9f2aab754004e2025-02-03T12:00:47ZengSAGE PublishingIndian Journal of Rheumatology0973-36980973-37012020-01-0115614515210.4103/injr.injr_80_20Sporadic inclusion body myositis in the rheumatology clinicFernando Henrique Carlos de SouzaGustavo Luiz Behrens PintoJean Marcos de SouzaPablo Arturo Olivo PalloLeonardo Santos HoffSamuel Katsuyuki ShinjoSporadic inclusion body myositis (sIBM) is a progressive and insidious skeletal muscle disorder characterized classically by the quadriceps, wrist, and finger flexor weakness. The main irreversible complications of sIBM are dysphagia and walking difficulties. The disease affects more men than women, and the symptom onset mainly occurs between 50 and 70 years of age. Due to its slow progression, sIBM diagnosis is frequently delayed and therefore misdiagnosed as other muscle diseases. sIBM remains refractory to treatment (e.g., glucocorticoid, and immunosuppressive/immunomodulatory/immunobiological drugs). Although there have been no robust clinical trials, training exercise/physiotherapy should be prescribed regularly in sIBM patients.http://www.indianjrheumatol.com/article.asp?issn=0973-3698;year=2020;volume=15;issue=6;spage=145;epage=152;aulast=deidiopathic inflammatory myopathiesinclusion body myositismyopathiesmyositisreview
spellingShingle Fernando Henrique Carlos de Souza
Gustavo Luiz Behrens Pinto
Jean Marcos de Souza
Pablo Arturo Olivo Pallo
Leonardo Santos Hoff
Samuel Katsuyuki Shinjo
Sporadic inclusion body myositis in the rheumatology clinic
Indian Journal of Rheumatology
idiopathic inflammatory myopathies
inclusion body myositis
myopathies
myositis
review
title Sporadic inclusion body myositis in the rheumatology clinic
title_full Sporadic inclusion body myositis in the rheumatology clinic
title_fullStr Sporadic inclusion body myositis in the rheumatology clinic
title_full_unstemmed Sporadic inclusion body myositis in the rheumatology clinic
title_short Sporadic inclusion body myositis in the rheumatology clinic
title_sort sporadic inclusion body myositis in the rheumatology clinic
topic idiopathic inflammatory myopathies
inclusion body myositis
myopathies
myositis
review
url http://www.indianjrheumatol.com/article.asp?issn=0973-3698;year=2020;volume=15;issue=6;spage=145;epage=152;aulast=de
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