Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRI
We report the case of a 15-year-old girl who presented with a 2-month history of severe fatigue and rapidly worsening myalgia. Biological tests revealed hypereosinophilia and an inflammatory syndrome. MRI showed increased signal intensity in the superficial and deep aponeurotic layers on T2-weighted...
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| Format: | Article |
| Language: | English |
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Elsevier
2025-03-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043324012305 |
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| author | Hadj Hsain Ihssan Ezzaky Sara Maslouhi Kaoutar Lahlou Chailmae Marrakchi Salma Allali Nazik Chat Latifa El Haddah Siham |
| author_facet | Hadj Hsain Ihssan Ezzaky Sara Maslouhi Kaoutar Lahlou Chailmae Marrakchi Salma Allali Nazik Chat Latifa El Haddah Siham |
| author_sort | Hadj Hsain Ihssan |
| collection | DOAJ |
| description | We report the case of a 15-year-old girl who presented with a 2-month history of severe fatigue and rapidly worsening myalgia. Biological tests revealed hypereosinophilia and an inflammatory syndrome. MRI showed increased signal intensity in the superficial and deep aponeurotic layers on T2-weighted images, with moderate fascia enhancement after contrast administration. A muscle biopsy of the arm was performed, revealing an accumulation of eosinophils in the muscle aponeuroses. Eosinophilic fasciitis (EF) is a rare connective tissue disorder characterized by inflammation of the fascia, leading to skin thickening and limb pain. While it predominantly affects adults, pediatric cases are rare, making diagnosis challenging due to its overlap with other fibrotic diseases. |
| format | Article |
| id | doaj-art-2bbac39a64a94208a0b26715413ee6e5 |
| institution | Kabale University |
| issn | 1930-0433 |
| language | English |
| publishDate | 2025-03-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj-art-2bbac39a64a94208a0b26715413ee6e52025-01-18T05:03:50ZengElsevierRadiology Case Reports1930-04332025-03-0120317601765Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRIHadj Hsain Ihssan0Ezzaky Sara1Maslouhi Kaoutar2Lahlou Chailmae3Marrakchi Salma4Allali Nazik5Chat Latifa6El Haddah Siham7Corresponding author.; Departement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoDepartement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoDepartement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoDepartement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoDepartement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoDepartement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoDepartement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoDepartement of radiology HER, University Mohammed V Rabat, Rabat, MoroccoWe report the case of a 15-year-old girl who presented with a 2-month history of severe fatigue and rapidly worsening myalgia. Biological tests revealed hypereosinophilia and an inflammatory syndrome. MRI showed increased signal intensity in the superficial and deep aponeurotic layers on T2-weighted images, with moderate fascia enhancement after contrast administration. A muscle biopsy of the arm was performed, revealing an accumulation of eosinophils in the muscle aponeuroses. Eosinophilic fasciitis (EF) is a rare connective tissue disorder characterized by inflammation of the fascia, leading to skin thickening and limb pain. While it predominantly affects adults, pediatric cases are rare, making diagnosis challenging due to its overlap with other fibrotic diseases.http://www.sciencedirect.com/science/article/pii/S1930043324012305Shulman's SyndromeEosinophilic FasciitisMRI |
| spellingShingle | Hadj Hsain Ihssan Ezzaky Sara Maslouhi Kaoutar Lahlou Chailmae Marrakchi Salma Allali Nazik Chat Latifa El Haddah Siham Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRI Radiology Case Reports Shulman's Syndrome Eosinophilic Fasciitis MRI |
| title | Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRI |
| title_full | Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRI |
| title_fullStr | Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRI |
| title_full_unstemmed | Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRI |
| title_short | Unraveling Shulman's syndrome: A rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on MRI |
| title_sort | unraveling shulman s syndrome a rare case of eosinophilic fasciitis in a pediatric patient with fascial abnormalities on mri |
| topic | Shulman's Syndrome Eosinophilic Fasciitis MRI |
| url | http://www.sciencedirect.com/science/article/pii/S1930043324012305 |
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