Solitary Mastocytoma in Pediatrics. Case Report and Literature Review

The mastocytoma is a genodermatosis of unknown etiology, so it is included in the group of rare or uncommon diseases; it usually appears in childhood or at birth. It is characterized by local or systemic accumulation of primed cells, which causes the appearance of persistent, pigmented and very itch...

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Main Authors: Juan Carlos Yanes Macías, Mery Rosa Betancourt Trujillo, Lino Arístides Sánchez Galván
Format: Article
Language:Spanish
Published: Universidad de las Ciencias Médicas de Cienfuegos 2020-02-01
Series:Revista Finlay
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Online Access:https://revfinlay.sld.cu/index.php/finlay/article/view/779
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author Juan Carlos Yanes Macías
Mery Rosa Betancourt Trujillo
Lino Arístides Sánchez Galván
author_facet Juan Carlos Yanes Macías
Mery Rosa Betancourt Trujillo
Lino Arístides Sánchez Galván
author_sort Juan Carlos Yanes Macías
collection DOAJ
description The mastocytoma is a genodermatosis of unknown etiology, so it is included in the group of rare or uncommon diseases; it usually appears in childhood or at birth. It is characterized by local or systemic accumulation of primed cells, which causes the appearance of persistent, pigmented and very itchy skin lesions with exclusive skin involvement, usually presents as a single lesion in the neck, trunk, arms and legs. Typical features are that of a reddish-brown or yellowish brown nodule, of gummy consistency, the surface looks like orange peel, and Darier's sign. The case of a 4-month-old infant with a diagnosis of solitary mastocytoma with Darier's sign is presented. This report is made due to the low frequency of this disease at the Paquito González Cueto de Cienfuegos University Pediatric Hospital. Currently the patient is monitored by dermatology specialists, with antihistamine treatment and mast cell stabilizer.
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institution Kabale University
issn 2221-2434
language Spanish
publishDate 2020-02-01
publisher Universidad de las Ciencias Médicas de Cienfuegos
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spelling doaj-art-2b668fdb2f65486d98d5a956965147ee2025-01-30T21:22:00ZspaUniversidad de las Ciencias Médicas de CienfuegosRevista Finlay2221-24342020-02-011014649435Solitary Mastocytoma in Pediatrics. Case Report and Literature ReviewJuan Carlos Yanes Macías0Mery Rosa Betancourt Trujillo1Lino Arístides Sánchez Galván2Hospital Pediátrico Universitario Paquito González Cueto. Cienfuegos.Hospital Pediátrico Universitario Paquito González Cueto. Cienfuegos.Hospital Pediátrico Universitario Paquito González Cueto. Cienfuegos.The mastocytoma is a genodermatosis of unknown etiology, so it is included in the group of rare or uncommon diseases; it usually appears in childhood or at birth. It is characterized by local or systemic accumulation of primed cells, which causes the appearance of persistent, pigmented and very itchy skin lesions with exclusive skin involvement, usually presents as a single lesion in the neck, trunk, arms and legs. Typical features are that of a reddish-brown or yellowish brown nodule, of gummy consistency, the surface looks like orange peel, and Darier's sign. The case of a 4-month-old infant with a diagnosis of solitary mastocytoma with Darier's sign is presented. This report is made due to the low frequency of this disease at the Paquito González Cueto de Cienfuegos University Pediatric Hospital. Currently the patient is monitored by dermatology specialists, with antihistamine treatment and mast cell stabilizer.https://revfinlay.sld.cu/index.php/finlay/article/view/779mastocitomaetiologíaenfermedades raras
spellingShingle Juan Carlos Yanes Macías
Mery Rosa Betancourt Trujillo
Lino Arístides Sánchez Galván
Solitary Mastocytoma in Pediatrics. Case Report and Literature Review
Revista Finlay
mastocitoma
etiología
enfermedades raras
title Solitary Mastocytoma in Pediatrics. Case Report and Literature Review
title_full Solitary Mastocytoma in Pediatrics. Case Report and Literature Review
title_fullStr Solitary Mastocytoma in Pediatrics. Case Report and Literature Review
title_full_unstemmed Solitary Mastocytoma in Pediatrics. Case Report and Literature Review
title_short Solitary Mastocytoma in Pediatrics. Case Report and Literature Review
title_sort solitary mastocytoma in pediatrics case report and literature review
topic mastocitoma
etiología
enfermedades raras
url https://revfinlay.sld.cu/index.php/finlay/article/view/779
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AT linoaristidessanchezgalvan solitarymastocytomainpediatricscasereportandliteraturereview