Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutants

Misfolding and aggregation of the neuronal protein alpha-synuclein (aSyn) has been identified as a hallmark of Parkinson’s disease (PD) pathology and other synucleinopathies. Preventing formation of intracellular aSyn accumulations constitutes a therapeutic strategy against disease development. We r...

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Main Authors: Linnea Charlotta Hjelm, Wojciech Paslawski, Christofer Lendel, Siri Flemming Svedmark, Per Svenningsson, Stefan Ståhl, Hanna Lindberg, John Löfblom
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-05-01
Series:Frontiers in Immunology
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Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2025.1574755/full
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author Linnea Charlotta Hjelm
Wojciech Paslawski
Christofer Lendel
Siri Flemming Svedmark
Per Svenningsson
Stefan Ståhl
Hanna Lindberg
John Löfblom
author_facet Linnea Charlotta Hjelm
Wojciech Paslawski
Christofer Lendel
Siri Flemming Svedmark
Per Svenningsson
Stefan Ståhl
Hanna Lindberg
John Löfblom
author_sort Linnea Charlotta Hjelm
collection DOAJ
description Misfolding and aggregation of the neuronal protein alpha-synuclein (aSyn) has been identified as a hallmark of Parkinson’s disease (PD) pathology and other synucleinopathies. Preventing formation of intracellular aSyn accumulations constitutes a therapeutic strategy against disease development. We recently reported on a new type of affinity protein, denoted Sequestrin, aimed for efficient and stable interactions with aggregation-prone amyloidogenic proteins and peptides. Upon binding, sequestrins interact with the aggregation-prone peptide and form a stabilizing four-stranded beta sheet with similarities to the beta sheet rich structures seen in amyloid fibrils. Here, high-affinity aSyn-binding sequestrins were isolated from a large naïve sequestrin library using phage display technology. The best binders demonstrated dissociation constant, KD, values in the 10 nM-range, and structural rearrangements in both the sequestrin and aSyn protein upon binding. Modelling using AlphaFold, followed by NMR spectroscopy suggested that the sequestrins bind an N-terminal region of aSyn that is critical for amyloidogenic aggregation. In an in vitro aggregation study, the sequestrins demonstrated complete inhibition of aSyn aggregation at equimolar concentrations, including the three familial mutants A30P, E46K, and A53T that are associated with Parkinson’s disease and Lewy body dementia.
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spelling doaj-art-2b6181bfb98b4ddb8d5df5dfa0083a4e2025-08-20T03:49:46ZengFrontiers Media S.A.Frontiers in Immunology1664-32242025-05-011610.3389/fimmu.2025.15747551574755Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutantsLinnea Charlotta Hjelm0Wojciech Paslawski1Christofer Lendel2Siri Flemming Svedmark3Per Svenningsson4Stefan Ståhl5Hanna Lindberg6John Löfblom7Department of Protein Science, School of Engineering Sciences in Chemistry, Biotechnology and Health, KTH Royal Institute of Technology, Stockholm, SwedenDepartment of Clinical Neuroscience, Karolinska Institute, Stockholm, SwedenDepartment of Chemistry, School of Engineering Sciences in Chemistry, Biotechnology and Health, KTH Royal Institute of Technology, Stockholm, SwedenDepartment of Protein Science, School of Engineering Sciences in Chemistry, Biotechnology and Health, KTH Royal Institute of Technology, Stockholm, SwedenDepartment of Clinical Neuroscience, Karolinska Institute, Stockholm, SwedenDepartment of Protein Science, School of Engineering Sciences in Chemistry, Biotechnology and Health, KTH Royal Institute of Technology, Stockholm, SwedenDepartment of Protein Science, School of Engineering Sciences in Chemistry, Biotechnology and Health, KTH Royal Institute of Technology, Stockholm, SwedenDepartment of Protein Science, School of Engineering Sciences in Chemistry, Biotechnology and Health, KTH Royal Institute of Technology, Stockholm, SwedenMisfolding and aggregation of the neuronal protein alpha-synuclein (aSyn) has been identified as a hallmark of Parkinson’s disease (PD) pathology and other synucleinopathies. Preventing formation of intracellular aSyn accumulations constitutes a therapeutic strategy against disease development. We recently reported on a new type of affinity protein, denoted Sequestrin, aimed for efficient and stable interactions with aggregation-prone amyloidogenic proteins and peptides. Upon binding, sequestrins interact with the aggregation-prone peptide and form a stabilizing four-stranded beta sheet with similarities to the beta sheet rich structures seen in amyloid fibrils. Here, high-affinity aSyn-binding sequestrins were isolated from a large naïve sequestrin library using phage display technology. The best binders demonstrated dissociation constant, KD, values in the 10 nM-range, and structural rearrangements in both the sequestrin and aSyn protein upon binding. Modelling using AlphaFold, followed by NMR spectroscopy suggested that the sequestrins bind an N-terminal region of aSyn that is critical for amyloidogenic aggregation. In an in vitro aggregation study, the sequestrins demonstrated complete inhibition of aSyn aggregation at equimolar concentrations, including the three familial mutants A30P, E46K, and A53T that are associated with Parkinson’s disease and Lewy body dementia.https://www.frontiersin.org/articles/10.3389/fimmu.2025.1574755/fullaffibody moleculealpha-synucleindirected evolutionParkinson’s diseasephage displaysequestrin
spellingShingle Linnea Charlotta Hjelm
Wojciech Paslawski
Christofer Lendel
Siri Flemming Svedmark
Per Svenningsson
Stefan Ståhl
Hanna Lindberg
John Löfblom
Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutants
Frontiers in Immunology
affibody molecule
alpha-synuclein
directed evolution
Parkinson’s disease
phage display
sequestrin
title Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutants
title_full Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutants
title_fullStr Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutants
title_full_unstemmed Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutants
title_short Engineered sequestrins inhibit aggregation of pathogenic alpha-synuclein mutants
title_sort engineered sequestrins inhibit aggregation of pathogenic alpha synuclein mutants
topic affibody molecule
alpha-synuclein
directed evolution
Parkinson’s disease
phage display
sequestrin
url https://www.frontiersin.org/articles/10.3389/fimmu.2025.1574755/full
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