Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser Syndrome

We report a case of adenomyosis which developed from a hypoplastic uterus and leiomyoma in a patient with MRKH syndrome. A 45-year-old Malay female with primary amenorrhoea and primary infertility presented with abdominal mass and abdominal pain. She is phenotypically female, has well developed seco...

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Main Authors: P. S. Hoo, A. R. Norhaslinda, J. N. Shah Reza
Format: Article
Language:English
Published: Wiley 2016-01-01
Series:Case Reports in Obstetrics and Gynecology
Online Access:http://dx.doi.org/10.1155/2016/3725043
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author P. S. Hoo
A. R. Norhaslinda
J. N. Shah Reza
author_facet P. S. Hoo
A. R. Norhaslinda
J. N. Shah Reza
author_sort P. S. Hoo
collection DOAJ
description We report a case of adenomyosis which developed from a hypoplastic uterus and leiomyoma in a patient with MRKH syndrome. A 45-year-old Malay female with primary amenorrhoea and primary infertility presented with abdominal mass and abdominal pain. She is phenotypically female, has well developed secondary sexual characteristics, and has normal female external genitalia with shallow vagina dimple. Transabdominal ultrasonography showed a homogenous adnexal mass of 10 × 8 cm, uterus sized 5 × 4 cm, and normal kidneys. A complex mass of right adnexa was demonstrated by CT scan. Exploratory laparotomy showed torsion of right adnexal mass and rudimentary uterus with fibroid but no endometrial tissue and blind end with absent cervix. The normal right ovary and tube were not visualized. The left fallopian tube and ovary were normal. It is also complicated by vaginal agenesis. Removal of right adnexal mass and rudimentary uterus was done with preservation of left ovary. The histologic diagnosis was uterine adenomyosis and leiomyoma arising from the right adnexa, possibly from the broad ligament.
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spelling doaj-art-2928bab695404660b757f57bda1aabfa2025-02-03T05:47:59ZengWileyCase Reports in Obstetrics and Gynecology2090-66842090-66922016-01-01201610.1155/2016/37250433725043Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser SyndromeP. S. Hoo0A. R. Norhaslinda1J. N. Shah Reza2Obstetrics & Gynaecology Department, School of Medical Science, Universiti Sains Malaysia, Kubang Kerian, Kelantan, MalaysiaObstetrics & Gynaecology Department, School of Medical Science, Universiti Sains Malaysia, Kubang Kerian, Kelantan, MalaysiaObstetrics & Gynaecology Department, School of Medical Science, Universiti Sains Malaysia, Kubang Kerian, Kelantan, MalaysiaWe report a case of adenomyosis which developed from a hypoplastic uterus and leiomyoma in a patient with MRKH syndrome. A 45-year-old Malay female with primary amenorrhoea and primary infertility presented with abdominal mass and abdominal pain. She is phenotypically female, has well developed secondary sexual characteristics, and has normal female external genitalia with shallow vagina dimple. Transabdominal ultrasonography showed a homogenous adnexal mass of 10 × 8 cm, uterus sized 5 × 4 cm, and normal kidneys. A complex mass of right adnexa was demonstrated by CT scan. Exploratory laparotomy showed torsion of right adnexal mass and rudimentary uterus with fibroid but no endometrial tissue and blind end with absent cervix. The normal right ovary and tube were not visualized. The left fallopian tube and ovary were normal. It is also complicated by vaginal agenesis. Removal of right adnexal mass and rudimentary uterus was done with preservation of left ovary. The histologic diagnosis was uterine adenomyosis and leiomyoma arising from the right adnexa, possibly from the broad ligament.http://dx.doi.org/10.1155/2016/3725043
spellingShingle P. S. Hoo
A. R. Norhaslinda
J. N. Shah Reza
Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser Syndrome
Case Reports in Obstetrics and Gynecology
title Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser Syndrome
title_full Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser Syndrome
title_fullStr Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser Syndrome
title_full_unstemmed Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser Syndrome
title_short Rare Case of Leiomyoma and Adenomyosis in Mayer-Rokitansky-Kuster-Hauser Syndrome
title_sort rare case of leiomyoma and adenomyosis in mayer rokitansky kuster hauser syndrome
url http://dx.doi.org/10.1155/2016/3725043
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