Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review

Rasmussen’s encephalitis (RE) is a rare progressive inflammatory disease of the central nervous system. It is characterized by unilateral hemispheric atrophy, pharmacoresistant focal seizures, and progressive neurological deficit. The exact etiopathogenesis still remains unknown. Brain imaging plays...

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Main Authors: Hedia Klaa, Thouraya Ben Younes, Hanene Benrhouma, Sonia Nagi, Aida Rouissi, Ichraf Kraoua, Ilhem Ben Youssef-Turki
Format: Article
Language:English
Published: Wiley 2020-01-01
Series:Case Reports in Neurological Medicine
Online Access:http://dx.doi.org/10.1155/2020/6810237
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author Hedia Klaa
Thouraya Ben Younes
Hanene Benrhouma
Sonia Nagi
Aida Rouissi
Ichraf Kraoua
Ilhem Ben Youssef-Turki
author_facet Hedia Klaa
Thouraya Ben Younes
Hanene Benrhouma
Sonia Nagi
Aida Rouissi
Ichraf Kraoua
Ilhem Ben Youssef-Turki
author_sort Hedia Klaa
collection DOAJ
description Rasmussen’s encephalitis (RE) is a rare progressive inflammatory disease of the central nervous system. It is characterized by unilateral hemispheric atrophy, pharmacoresistant focal seizures, and progressive neurological deficit. The exact etiopathogenesis still remains unknown. Brain imaging plays an important role in diagnosis and follow-up. Fluctuation of lesions in brain imaging was reported in few cases. Herein, we report an additional pediatric case of Rasmussen encephalitis with fluctuating changes in brain MRI.
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institution Kabale University
issn 2090-6668
2090-6676
language English
publishDate 2020-01-01
publisher Wiley
record_format Article
series Case Reports in Neurological Medicine
spelling doaj-art-27181193de8146b59e490f00664dab272025-02-03T01:04:47ZengWileyCase Reports in Neurological Medicine2090-66682090-66762020-01-01202010.1155/2020/68102376810237Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature ReviewHedia Klaa0Thouraya Ben Younes1Hanene Benrhouma2Sonia Nagi3Aida Rouissi4Ichraf Kraoua5Ilhem Ben Youssef-Turki6Department of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaUniversity of Tunis El Manar, Faculty of Medicine of Tunis, Tunis 1007, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaRasmussen’s encephalitis (RE) is a rare progressive inflammatory disease of the central nervous system. It is characterized by unilateral hemispheric atrophy, pharmacoresistant focal seizures, and progressive neurological deficit. The exact etiopathogenesis still remains unknown. Brain imaging plays an important role in diagnosis and follow-up. Fluctuation of lesions in brain imaging was reported in few cases. Herein, we report an additional pediatric case of Rasmussen encephalitis with fluctuating changes in brain MRI.http://dx.doi.org/10.1155/2020/6810237
spellingShingle Hedia Klaa
Thouraya Ben Younes
Hanene Benrhouma
Sonia Nagi
Aida Rouissi
Ichraf Kraoua
Ilhem Ben Youssef-Turki
Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review
Case Reports in Neurological Medicine
title Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review
title_full Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review
title_fullStr Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review
title_full_unstemmed Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review
title_short Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review
title_sort rasmussen s encephalitis a report of a tunisian pediatric case and literature review
url http://dx.doi.org/10.1155/2020/6810237
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