Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review
Rasmussen’s encephalitis (RE) is a rare progressive inflammatory disease of the central nervous system. It is characterized by unilateral hemispheric atrophy, pharmacoresistant focal seizures, and progressive neurological deficit. The exact etiopathogenesis still remains unknown. Brain imaging plays...
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Format: | Article |
Language: | English |
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Wiley
2020-01-01
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Series: | Case Reports in Neurological Medicine |
Online Access: | http://dx.doi.org/10.1155/2020/6810237 |
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author | Hedia Klaa Thouraya Ben Younes Hanene Benrhouma Sonia Nagi Aida Rouissi Ichraf Kraoua Ilhem Ben Youssef-Turki |
author_facet | Hedia Klaa Thouraya Ben Younes Hanene Benrhouma Sonia Nagi Aida Rouissi Ichraf Kraoua Ilhem Ben Youssef-Turki |
author_sort | Hedia Klaa |
collection | DOAJ |
description | Rasmussen’s encephalitis (RE) is a rare progressive inflammatory disease of the central nervous system. It is characterized by unilateral hemispheric atrophy, pharmacoresistant focal seizures, and progressive neurological deficit. The exact etiopathogenesis still remains unknown. Brain imaging plays an important role in diagnosis and follow-up. Fluctuation of lesions in brain imaging was reported in few cases. Herein, we report an additional pediatric case of Rasmussen encephalitis with fluctuating changes in brain MRI. |
format | Article |
id | doaj-art-27181193de8146b59e490f00664dab27 |
institution | Kabale University |
issn | 2090-6668 2090-6676 |
language | English |
publishDate | 2020-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Neurological Medicine |
spelling | doaj-art-27181193de8146b59e490f00664dab272025-02-03T01:04:47ZengWileyCase Reports in Neurological Medicine2090-66682090-66762020-01-01202010.1155/2020/68102376810237Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature ReviewHedia Klaa0Thouraya Ben Younes1Hanene Benrhouma2Sonia Nagi3Aida Rouissi4Ichraf Kraoua5Ilhem Ben Youssef-Turki6Department of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaUniversity of Tunis El Manar, Faculty of Medicine of Tunis, Tunis 1007, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaDepartment of Child and Adolescent Neurology, Research Laboratory LR18SP04, National Institute Mongi Ben Hmida of Neurology, Tunis, TunisiaRasmussen’s encephalitis (RE) is a rare progressive inflammatory disease of the central nervous system. It is characterized by unilateral hemispheric atrophy, pharmacoresistant focal seizures, and progressive neurological deficit. The exact etiopathogenesis still remains unknown. Brain imaging plays an important role in diagnosis and follow-up. Fluctuation of lesions in brain imaging was reported in few cases. Herein, we report an additional pediatric case of Rasmussen encephalitis with fluctuating changes in brain MRI.http://dx.doi.org/10.1155/2020/6810237 |
spellingShingle | Hedia Klaa Thouraya Ben Younes Hanene Benrhouma Sonia Nagi Aida Rouissi Ichraf Kraoua Ilhem Ben Youssef-Turki Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review Case Reports in Neurological Medicine |
title | Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review |
title_full | Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review |
title_fullStr | Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review |
title_full_unstemmed | Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review |
title_short | Rasmussen’s Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review |
title_sort | rasmussen s encephalitis a report of a tunisian pediatric case and literature review |
url | http://dx.doi.org/10.1155/2020/6810237 |
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