Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child
Malignant peripheral nerve sheath tumors (MPNSTs) are nonrhabdomyosarcoma soft tissue sarcomas with rare occurrence in children specially in the retroperitoneum. We describe a young child who presented with an abdominal mass. Both ultrasound and computed tomography revealed a large right-sided abdom...
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| Format: | Article |
| Language: | English |
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Wiley
2013-01-01
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| Series: | Case Reports in Oncological Medicine |
| Online Access: | http://dx.doi.org/10.1155/2013/627472 |
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| author | Samin Alavi M. T. Arzanian Yalda Nilipour |
| author_facet | Samin Alavi M. T. Arzanian Yalda Nilipour |
| author_sort | Samin Alavi |
| collection | DOAJ |
| description | Malignant peripheral nerve sheath tumors (MPNSTs) are nonrhabdomyosarcoma soft tissue sarcomas with rare occurrence in children specially in the retroperitoneum. We describe a young child who presented with an abdominal mass. Both ultrasound and computed tomography revealed a large right-sided abdominal mass in the anatomic place of right kidney, while no kidney or ureter was observed at that side. He underwent surgical resection of the tumor with a primary impression of Wilms tumor. To the authors’ knowledge, this is the first case of retroperitoneal malignant peripheral nerve sheath tumor and absent kidney. This case suggests the very rare probability of association of MPNSTs in children with genitourinary tract anomalies such as renal agenesis. |
| format | Article |
| id | doaj-art-23233c76403949e7a84249b0ad7e693b |
| institution | Kabale University |
| issn | 2090-6706 2090-6714 |
| language | English |
| publishDate | 2013-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Oncological Medicine |
| spelling | doaj-art-23233c76403949e7a84249b0ad7e693b2025-02-03T01:30:18ZengWileyCase Reports in Oncological Medicine2090-67062090-67142013-01-01201310.1155/2013/627472627472Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a ChildSamin Alavi0M. T. Arzanian1Yalda Nilipour2Pediatric Congenital Hematologic Disorders Research Center, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, IranPediatric Congenital Hematologic Disorders Research Center, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, IranPediatric Pathology Research Center, Mofid Children’s Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, IranMalignant peripheral nerve sheath tumors (MPNSTs) are nonrhabdomyosarcoma soft tissue sarcomas with rare occurrence in children specially in the retroperitoneum. We describe a young child who presented with an abdominal mass. Both ultrasound and computed tomography revealed a large right-sided abdominal mass in the anatomic place of right kidney, while no kidney or ureter was observed at that side. He underwent surgical resection of the tumor with a primary impression of Wilms tumor. To the authors’ knowledge, this is the first case of retroperitoneal malignant peripheral nerve sheath tumor and absent kidney. This case suggests the very rare probability of association of MPNSTs in children with genitourinary tract anomalies such as renal agenesis.http://dx.doi.org/10.1155/2013/627472 |
| spellingShingle | Samin Alavi M. T. Arzanian Yalda Nilipour Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child Case Reports in Oncological Medicine |
| title | Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child |
| title_full | Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child |
| title_fullStr | Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child |
| title_full_unstemmed | Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child |
| title_short | Retroperitoneal Malignant Peripheral Nerve Sheath Tumor Replacing an Absent Kidney in a Child |
| title_sort | retroperitoneal malignant peripheral nerve sheath tumor replacing an absent kidney in a child |
| url | http://dx.doi.org/10.1155/2013/627472 |
| work_keys_str_mv | AT saminalavi retroperitonealmalignantperipheralnervesheathtumorreplacinganabsentkidneyinachild AT mtarzanian retroperitonealmalignantperipheralnervesheathtumorreplacinganabsentkidneyinachild AT yaldanilipour retroperitonealmalignantperipheralnervesheathtumorreplacinganabsentkidneyinachild |