Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia
Portal vein aneurisym (PVA), peliosis hepatis (PH) and intestinal lymphangiectasia (IL) all are very uncommon entities. Herein, we presented a unique patient with these three rare entities who was admitted to our hospital because of portal hypertensive ascites rich in protein and lymphocyte. PVA was...
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| Format: | Article |
| Language: | English |
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Wiley
2009-01-01
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| Series: | Gastroenterology Research and Practice |
| Online Access: | http://dx.doi.org/10.1155/2009/479264 |
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| author | Zeynel Mungan Binnur Pinarbasi Baris Bakir Mine Gulluoglu Bulent Baran Filiz Akyuz Kadir Demir Sabahattin Kaymakoglu |
| author_facet | Zeynel Mungan Binnur Pinarbasi Baris Bakir Mine Gulluoglu Bulent Baran Filiz Akyuz Kadir Demir Sabahattin Kaymakoglu |
| author_sort | Zeynel Mungan |
| collection | DOAJ |
| description | Portal vein aneurisym (PVA), peliosis hepatis (PH) and intestinal lymphangiectasia (IL) all are very uncommon entities. Herein, we presented a unique patient with these three rare entities who was admitted to our hospital because of portal hypertensive ascites rich in protein and lymphocyte. PVA was extrahepatic and associated with coronary vein aneurysm. Peliosis hepatis was of microscopic form. Lymphangiectasia was present in peritoneum and small intestine. Diagnoses of these rare entities were made by imaging techniques and histopathological findings. Patient also had hydronephrosis caused by ureteropelvic junction narrowing. Best of our knowledge, there is no such a case reported previously with the association of PVA, PH and IL. Therefore, we propose PVAPHIL syndrome to define this novel association. |
| format | Article |
| id | doaj-art-206f27e5bbec4f4ba7d7e3d2b67aca71 |
| institution | Kabale University |
| issn | 1687-6121 1687-630X |
| language | English |
| publishDate | 2009-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Gastroenterology Research and Practice |
| spelling | doaj-art-206f27e5bbec4f4ba7d7e3d2b67aca712025-02-03T07:25:33ZengWileyGastroenterology Research and Practice1687-61211687-630X2009-01-01200910.1155/2009/479264479264Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal LymphangiectasiaZeynel Mungan0Binnur Pinarbasi1Baris Bakir2Mine Gulluoglu3Bulent Baran4Filiz Akyuz5Kadir Demir6Sabahattin Kaymakoglu7Department of Gastroenterohepatology, Istanbul Medical Faculty, Istanbul University, Millet Cad. 34390 Capa, Istanbul, TurkeyDepartment of Gastroenterohepatology, Istanbul Medical Faculty, Istanbul University, Millet Cad. 34390 Capa, Istanbul, TurkeyDepartment of Radiology, Istanbul Medical Faculty, Istanbul University, Istanbul, TurkeyDepartment of Pathology, Istanbul Medical Faculty, Istanbul University, Istanbul, TurkeyDepartment of Gastroenterohepatology, Istanbul Medical Faculty, Istanbul University, Millet Cad. 34390 Capa, Istanbul, TurkeyDepartment of Gastroenterohepatology, Istanbul Medical Faculty, Istanbul University, Millet Cad. 34390 Capa, Istanbul, TurkeyDepartment of Gastroenterohepatology, Istanbul Medical Faculty, Istanbul University, Millet Cad. 34390 Capa, Istanbul, TurkeyDepartment of Gastroenterohepatology, Istanbul Medical Faculty, Istanbul University, Millet Cad. 34390 Capa, Istanbul, TurkeyPortal vein aneurisym (PVA), peliosis hepatis (PH) and intestinal lymphangiectasia (IL) all are very uncommon entities. Herein, we presented a unique patient with these three rare entities who was admitted to our hospital because of portal hypertensive ascites rich in protein and lymphocyte. PVA was extrahepatic and associated with coronary vein aneurysm. Peliosis hepatis was of microscopic form. Lymphangiectasia was present in peritoneum and small intestine. Diagnoses of these rare entities were made by imaging techniques and histopathological findings. Patient also had hydronephrosis caused by ureteropelvic junction narrowing. Best of our knowledge, there is no such a case reported previously with the association of PVA, PH and IL. Therefore, we propose PVAPHIL syndrome to define this novel association.http://dx.doi.org/10.1155/2009/479264 |
| spellingShingle | Zeynel Mungan Binnur Pinarbasi Baris Bakir Mine Gulluoglu Bulent Baran Filiz Akyuz Kadir Demir Sabahattin Kaymakoglu Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia Gastroenterology Research and Practice |
| title | Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia |
| title_full | Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia |
| title_fullStr | Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia |
| title_full_unstemmed | Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia |
| title_short | Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia |
| title_sort | congenital portal vein aneurysm associated with peliosis hepatis and intestinal lymphangiectasia |
| url | http://dx.doi.org/10.1155/2009/479264 |
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