Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos Syndrome

This is a unique case of a female patient with features of classical and hypermobile types of Ehlers-Danlos syndrome (EDS) who developed complex scapular winging from spinal accessory and long thoracic neuropathies. These neurological problems became manifest after an uncomplicated total shoulder ar...

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Main Authors: John G. Skedros, Colton M. Phippen, Tanner D. Langston, Chad S. Mears, Amy L. Trujillo, Robert M. Miska
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:Case Reports in Orthopedics
Online Access:http://dx.doi.org/10.1155/2015/680252
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author John G. Skedros
Colton M. Phippen
Tanner D. Langston
Chad S. Mears
Amy L. Trujillo
Robert M. Miska
author_facet John G. Skedros
Colton M. Phippen
Tanner D. Langston
Chad S. Mears
Amy L. Trujillo
Robert M. Miska
author_sort John G. Skedros
collection DOAJ
description This is a unique case of a female patient with features of classical and hypermobile types of Ehlers-Danlos syndrome (EDS) who developed complex scapular winging from spinal accessory and long thoracic neuropathies. These neurological problems became manifest after an uncomplicated total shoulder arthroplasty (TSA). The patient had a complex postoperative course with extensive work-up in addition to revision shoulder surgery and manipulations to treat shoulder stiffness. It was eventually suspected that the periscapular nerve impairments occurred during physical therapy sessions after her TSA. This interpretation was further supported by genetic evidence that, in addition to EDS, the patient had an unrecognized genetic propensity for nerve palsies from stretch or pressure (“hereditary neuropathy with liability to pressure palsies” (HNPP)). By two years after the TSA the neuropathies had only partially improved, leaving the patient with persistent scapular winging and shoulder weakness. With this case we alert surgeons and physical therapists that patients with EDS can have not only a complicated course after TSA, but rare concurrent conditions that can further increase the propensity of neurological injuries that result in compromised shoulder function.
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spelling doaj-art-1d41fdefe10947ff9bfaade714461eb92025-02-03T05:57:57ZengWileyCase Reports in Orthopedics2090-67492090-67572015-01-01201510.1155/2015/680252680252Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos SyndromeJohn G. Skedros0Colton M. Phippen1Tanner D. Langston2Chad S. Mears3Amy L. Trujillo4Robert M. Miska5Department of Orthopaedic Surgery, The University of Utah, Salt Lake City, UT 84108, USAUtah Orthopaedic Specialists, Salt Lake City, UT 84107, USAUtah Orthopaedic Specialists, Salt Lake City, UT 84107, USAUtah Orthopaedic Specialists, Salt Lake City, UT 84107, USAOne to One Physical Therapy, Sandy, UT 84070, USARocky Mountain Neurological Associates, Salt Lake City, UT 84103, USAThis is a unique case of a female patient with features of classical and hypermobile types of Ehlers-Danlos syndrome (EDS) who developed complex scapular winging from spinal accessory and long thoracic neuropathies. These neurological problems became manifest after an uncomplicated total shoulder arthroplasty (TSA). The patient had a complex postoperative course with extensive work-up in addition to revision shoulder surgery and manipulations to treat shoulder stiffness. It was eventually suspected that the periscapular nerve impairments occurred during physical therapy sessions after her TSA. This interpretation was further supported by genetic evidence that, in addition to EDS, the patient had an unrecognized genetic propensity for nerve palsies from stretch or pressure (“hereditary neuropathy with liability to pressure palsies” (HNPP)). By two years after the TSA the neuropathies had only partially improved, leaving the patient with persistent scapular winging and shoulder weakness. With this case we alert surgeons and physical therapists that patients with EDS can have not only a complicated course after TSA, but rare concurrent conditions that can further increase the propensity of neurological injuries that result in compromised shoulder function.http://dx.doi.org/10.1155/2015/680252
spellingShingle John G. Skedros
Colton M. Phippen
Tanner D. Langston
Chad S. Mears
Amy L. Trujillo
Robert M. Miska
Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos Syndrome
Case Reports in Orthopedics
title Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos Syndrome
title_full Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos Syndrome
title_fullStr Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos Syndrome
title_full_unstemmed Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos Syndrome
title_short Complex Scapular Winging following Total Shoulder Arthroplasty in a Patient with Ehlers-Danlos Syndrome
title_sort complex scapular winging following total shoulder arthroplasty in a patient with ehlers danlos syndrome
url http://dx.doi.org/10.1155/2015/680252
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