A Case of Granulomatosis with Polyangiitis in Pregnancy

Granulomatosis with polyangiitis, a rare autoimmune disease affecting organs such as the respiratory system, kidneys, and lungs, poses unique challenges in pregnancy. A 25-year-old woman with chronic liver disease, vasculitis, protein C and S deficiency, hypothyroidism, and gestational diabetes pre...

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Main Authors: Rashid Naseem Khan, Aliya Naseem, Muhammad Athar Khan, Qurat ul Ain Qurat ul Ain, Mamoona Hashim, Hafiza Laila Hashim Khan
Format: Article
Language:English
Published: ziauddin University 2025-01-01
Series:Pakistan Journal of Medicine and Dentistry
Subjects:
Online Access:https://ojs.zu.edu.pk/pjmd/article/view/3334
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author Rashid Naseem Khan
Aliya Naseem
Muhammad Athar Khan
Qurat ul Ain Qurat ul Ain
Mamoona Hashim
Hafiza Laila Hashim Khan
author_facet Rashid Naseem Khan
Aliya Naseem
Muhammad Athar Khan
Qurat ul Ain Qurat ul Ain
Mamoona Hashim
Hafiza Laila Hashim Khan
author_sort Rashid Naseem Khan
collection DOAJ
description Granulomatosis with polyangiitis, a rare autoimmune disease affecting organs such as the respiratory system, kidneys, and lungs, poses unique challenges in pregnancy. A 25-year-old woman with chronic liver disease, vasculitis, protein C and S deficiency, hypothyroidism, and gestational diabetes presented at 24 weeks gestation with shortness of breath, fever, and vomiting. Her thrombocytopenia was managed with transfusions, and regular prenatal ultrasounds were conducted. At 36 weeks, an elective cesarean delivered a healthy 2.4 kg baby. This case highlights the critical role of multidisciplinary care in achieving favorable outcomes in complex pregnancies affected by granulomatosis with polyangiitis.
format Article
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institution Kabale University
issn 2313-7371
2308-2593
language English
publishDate 2025-01-01
publisher ziauddin University
record_format Article
series Pakistan Journal of Medicine and Dentistry
spelling doaj-art-11e767811ca4400fa55a699c84c311182025-01-19T20:18:26Zengziauddin UniversityPakistan Journal of Medicine and Dentistry2313-73712308-25932025-01-0114110.36283/ziun-pjmd14-1/025A Case of Granulomatosis with Polyangiitis in PregnancyRashid Naseem Khan0Aliya Naseem1Muhammad Athar Khan2Qurat ul Ain Qurat ul Ain3Mamoona Hashim4 Hafiza Laila Hashim Khan5Liaquat College of Medicine & Dentistry, Karachi, PakistanLiaquat University of Medical and Health Sciences, Jamshoro, Sindh, PakistanLiaquat University of Medical and Health Sciences, Jamshoro, Sindh, PakistanLiaquat University of Medical and Health Sciences, Jamshoro, Sindh, PakistanLiaquat College of Medicine & Dentistry, Karachi, PakistanAga Khan University Hospital Karachi, Pakistan. Granulomatosis with polyangiitis, a rare autoimmune disease affecting organs such as the respiratory system, kidneys, and lungs, poses unique challenges in pregnancy. A 25-year-old woman with chronic liver disease, vasculitis, protein C and S deficiency, hypothyroidism, and gestational diabetes presented at 24 weeks gestation with shortness of breath, fever, and vomiting. Her thrombocytopenia was managed with transfusions, and regular prenatal ultrasounds were conducted. At 36 weeks, an elective cesarean delivered a healthy 2.4 kg baby. This case highlights the critical role of multidisciplinary care in achieving favorable outcomes in complex pregnancies affected by granulomatosis with polyangiitis. https://ojs.zu.edu.pk/pjmd/article/view/3334Granulomatosis with PolyangiitisWegener’ GranulomatosisGranulomatous VasculitisANCA-Associated VasculitisPregnancy
spellingShingle Rashid Naseem Khan
Aliya Naseem
Muhammad Athar Khan
Qurat ul Ain Qurat ul Ain
Mamoona Hashim
Hafiza Laila Hashim Khan
A Case of Granulomatosis with Polyangiitis in Pregnancy
Pakistan Journal of Medicine and Dentistry
Granulomatosis with Polyangiitis
Wegener’ Granulomatosis
Granulomatous Vasculitis
ANCA-Associated Vasculitis
Pregnancy
title A Case of Granulomatosis with Polyangiitis in Pregnancy
title_full A Case of Granulomatosis with Polyangiitis in Pregnancy
title_fullStr A Case of Granulomatosis with Polyangiitis in Pregnancy
title_full_unstemmed A Case of Granulomatosis with Polyangiitis in Pregnancy
title_short A Case of Granulomatosis with Polyangiitis in Pregnancy
title_sort case of granulomatosis with polyangiitis in pregnancy
topic Granulomatosis with Polyangiitis
Wegener’ Granulomatosis
Granulomatous Vasculitis
ANCA-Associated Vasculitis
Pregnancy
url https://ojs.zu.edu.pk/pjmd/article/view/3334
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