Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood

We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplas...

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Main Authors: Giovanni Ferlan, Claudio De Pasquale, Concetta Losito, Annalisa Fiorella, Nicola Marraudino, Francesco Tunzi
Format: Article
Language:English
Published: Wiley 2009-01-01
Series:Cardiology Research and Practice
Online Access:http://dx.doi.org/10.4061/2009/976190
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author Giovanni Ferlan
Claudio De Pasquale
Concetta Losito
Annalisa Fiorella
Nicola Marraudino
Francesco Tunzi
author_facet Giovanni Ferlan
Claudio De Pasquale
Concetta Losito
Annalisa Fiorella
Nicola Marraudino
Francesco Tunzi
author_sort Giovanni Ferlan
collection DOAJ
description We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.
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spelling doaj-art-0e0c37fbcb9c4bd0a91cbd627da703242025-02-03T01:10:23ZengWileyCardiology Research and Practice2090-05972009-01-01200910.4061/2009/976190976190Diffuse Supravalvular Aortic Stenosis: Surgical Repair in AdulthoodGiovanni Ferlan0Claudio De Pasquale1Concetta Losito2Annalisa Fiorella3Nicola Marraudino4Francesco Tunzi5Department of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyWe present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.http://dx.doi.org/10.4061/2009/976190
spellingShingle Giovanni Ferlan
Claudio De Pasquale
Concetta Losito
Annalisa Fiorella
Nicola Marraudino
Francesco Tunzi
Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
Cardiology Research and Practice
title Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
title_full Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
title_fullStr Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
title_full_unstemmed Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
title_short Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
title_sort diffuse supravalvular aortic stenosis surgical repair in adulthood
url http://dx.doi.org/10.4061/2009/976190
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