Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood
We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplas...
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Language: | English |
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Wiley
2009-01-01
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Series: | Cardiology Research and Practice |
Online Access: | http://dx.doi.org/10.4061/2009/976190 |
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author | Giovanni Ferlan Claudio De Pasquale Concetta Losito Annalisa Fiorella Nicola Marraudino Francesco Tunzi |
author_facet | Giovanni Ferlan Claudio De Pasquale Concetta Losito Annalisa Fiorella Nicola Marraudino Francesco Tunzi |
author_sort | Giovanni Ferlan |
collection | DOAJ |
description | We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta. |
format | Article |
id | doaj-art-0e0c37fbcb9c4bd0a91cbd627da70324 |
institution | Kabale University |
issn | 2090-0597 |
language | English |
publishDate | 2009-01-01 |
publisher | Wiley |
record_format | Article |
series | Cardiology Research and Practice |
spelling | doaj-art-0e0c37fbcb9c4bd0a91cbd627da703242025-02-03T01:10:23ZengWileyCardiology Research and Practice2090-05972009-01-01200910.4061/2009/976190976190Diffuse Supravalvular Aortic Stenosis: Surgical Repair in AdulthoodGiovanni Ferlan0Claudio De Pasquale1Concetta Losito2Annalisa Fiorella3Nicola Marraudino4Francesco Tunzi5Department of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyDepartment of Cardiac Surgery, University of Bari Medical School, Piazza Giulio Cesare 11, Bari 70122, ItalyWe present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.http://dx.doi.org/10.4061/2009/976190 |
spellingShingle | Giovanni Ferlan Claudio De Pasquale Concetta Losito Annalisa Fiorella Nicola Marraudino Francesco Tunzi Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood Cardiology Research and Practice |
title | Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood |
title_full | Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood |
title_fullStr | Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood |
title_full_unstemmed | Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood |
title_short | Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood |
title_sort | diffuse supravalvular aortic stenosis surgical repair in adulthood |
url | http://dx.doi.org/10.4061/2009/976190 |
work_keys_str_mv | AT giovanniferlan diffusesupravalvularaorticstenosissurgicalrepairinadulthood AT claudiodepasquale diffusesupravalvularaorticstenosissurgicalrepairinadulthood AT concettalosito diffusesupravalvularaorticstenosissurgicalrepairinadulthood AT annalisafiorella diffusesupravalvularaorticstenosissurgicalrepairinadulthood AT nicolamarraudino diffusesupravalvularaorticstenosissurgicalrepairinadulthood AT francescotunzi diffusesupravalvularaorticstenosissurgicalrepairinadulthood |