Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature
Rhabdomyoblastic differentiation in a malignant peripheral nerve sheath tumor (MPNST) is termed malignant triton tumor (MTT), a rare neoplasm that poses a diagnostic dilemma in the differential diagnosis of neck masses and portends poor prognosis. We report a sporadic case of MTT of the neck in a 23...
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| Format: | Article |
| Language: | English |
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Wiley
2014-01-01
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| Series: | Case Reports in Pathology |
| Online Access: | http://dx.doi.org/10.1155/2014/674094 |
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| author | Taissir Omar Hanaa Raslan Sahar El Sheikh Moataz Rizq Awatef Draz |
| author_facet | Taissir Omar Hanaa Raslan Sahar El Sheikh Moataz Rizq Awatef Draz |
| author_sort | Taissir Omar |
| collection | DOAJ |
| description | Rhabdomyoblastic differentiation in a malignant peripheral nerve sheath tumor (MPNST) is termed malignant triton tumor (MTT), a rare neoplasm that poses a diagnostic dilemma in the differential diagnosis of neck masses and portends poor prognosis. We report a sporadic case of MTT of the neck in a 23-year-old female. We present the pathological findings. Immunohistochemistry confirmed the neurogenic origin with S-100 expression and the rhabdomyoblastic differentiation with desmin and vimentin positivity. Radical surgical excision was done. After 4 years there were no signs of recurrence or distant metastasis. The clinical, microscopic, and long-term follow-up of this case are consistent with those of a low-grade malignancy. |
| format | Article |
| id | doaj-art-0be1456069e541ffac17184a669b5762 |
| institution | Kabale University |
| issn | 2090-6781 2090-679X |
| language | English |
| publishDate | 2014-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pathology |
| spelling | doaj-art-0be1456069e541ffac17184a669b57622025-02-03T06:15:11ZengWileyCase Reports in Pathology2090-67812090-679X2014-01-01201410.1155/2014/674094674094Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the LiteratureTaissir Omar0Hanaa Raslan1Sahar El Sheikh2Moataz Rizq3Awatef Draz4Oral Pathology Department, Faculty of Dentistry, Alexandria University, Champollion Street, Azarita, Alexandria 21526, EgyptOral Pathology Department, Faculty of Dentistry, Alexandria University, Champollion Street, Azarita, Alexandria 21526, EgyptOral Pathology Department, Faculty of Dentistry, Alexandria University, Champollion Street, Azarita, Alexandria 21526, EgyptMaxillofacial and Plastic Surgery Department, Faculty of Dentistry, Alexandria University, Champollion Street, Azarita, Alexandria 21526, EgyptOral Pathology Department, Faculty of Dentistry, King Abdulaziz University, P.O. Box 80200, Zip Code 21589, Jeddah 22252, Saudi ArabiaRhabdomyoblastic differentiation in a malignant peripheral nerve sheath tumor (MPNST) is termed malignant triton tumor (MTT), a rare neoplasm that poses a diagnostic dilemma in the differential diagnosis of neck masses and portends poor prognosis. We report a sporadic case of MTT of the neck in a 23-year-old female. We present the pathological findings. Immunohistochemistry confirmed the neurogenic origin with S-100 expression and the rhabdomyoblastic differentiation with desmin and vimentin positivity. Radical surgical excision was done. After 4 years there were no signs of recurrence or distant metastasis. The clinical, microscopic, and long-term follow-up of this case are consistent with those of a low-grade malignancy.http://dx.doi.org/10.1155/2014/674094 |
| spellingShingle | Taissir Omar Hanaa Raslan Sahar El Sheikh Moataz Rizq Awatef Draz Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature Case Reports in Pathology |
| title | Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature |
| title_full | Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature |
| title_fullStr | Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature |
| title_full_unstemmed | Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature |
| title_short | Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature |
| title_sort | low grade malignant triton tumor of the neck a case report and review of the literature |
| url | http://dx.doi.org/10.1155/2014/674094 |
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