Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review

Hepatic epithelioid angiomyolipoma is a rare mesenchymal liver tumor within the perivascular epithelioid cell tumor family, known for its uncertain malignancy and potential for aggressive behavior. Clinical presentation, laboratory findings, and imaging results lack specificity, making pathological...

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Main Authors: Da Teng, Yue Xu, Qingtao Meng, Qingsong Yang
Format: Article
Language:English
Published: SAGE Publishing 2025-01-01
Series:SAGE Open Medical Case Reports
Online Access:https://doi.org/10.1177/2050313X251314072
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author Da Teng
Yue Xu
Qingtao Meng
Qingsong Yang
author_facet Da Teng
Yue Xu
Qingtao Meng
Qingsong Yang
author_sort Da Teng
collection DOAJ
description Hepatic epithelioid angiomyolipoma is a rare mesenchymal liver tumor within the perivascular epithelioid cell tumor family, known for its uncertain malignancy and potential for aggressive behavior. Clinical presentation, laboratory findings, and imaging results lack specificity, making pathological examination critical for definitive diagnosis. This case report presents a 61-year-old male patient with a single tumor in the right liver lobe, measuring approximately 101 mm × 99 mm. Initial imaging misdiagnosed the mass as hepatocellular carcinoma. Following multidisciplinary treatment discussions and subsequent tumor resection, histopathology and immunohistochemistry confirmed hepatic epithelioid angiomyolipoma. Accurate diagnosis of hepatic epithelioid angiomyolipoma is challenging, relying on histopathological examination and immunohistochemistry as diagnostic standards. Continuous monitoring of patients with hepatic epithelioid angiomyolipoma over an extended period is deemed essential. This report highlights the positive impact of multidisciplinary treatment in diagnosing and managing hepatic epithelioid angiomyolipoma.
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institution Kabale University
issn 2050-313X
language English
publishDate 2025-01-01
publisher SAGE Publishing
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series SAGE Open Medical Case Reports
spelling doaj-art-0a3ca1607a2f4027affc2d7369a940e12025-01-20T07:03:27ZengSAGE PublishingSAGE Open Medical Case Reports2050-313X2025-01-011310.1177/2050313X251314072Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature reviewDa Teng0Yue Xu1Qingtao Meng2Qingsong Yang3Department of Hepatobiliary Pancreatic and Splenic Surgery Ward Ⅰ, The Affiliated ChuZhou Hospital of Anhui Medical University (The First People’s Hospital of Chuzhou), ChuZhou, ChinaDepartment of Ultrasound Medicine, The Affiliated ChuZhou Hospital of Anhui Medical University (The First People’s Hospital of Chuzhou), ChuZhou, ChinaDepartment of Radiology, The Affiliated ChuZhou Hospital of Anhui Medical University (The First People’s Hospital of Chuzhou), ChuZhou, ChinaDepartment of Hepatobiliary Pancreatic and Splenic Surgery Ward Ⅰ, The Affiliated ChuZhou Hospital of Anhui Medical University (The First People’s Hospital of Chuzhou), ChuZhou, ChinaHepatic epithelioid angiomyolipoma is a rare mesenchymal liver tumor within the perivascular epithelioid cell tumor family, known for its uncertain malignancy and potential for aggressive behavior. Clinical presentation, laboratory findings, and imaging results lack specificity, making pathological examination critical for definitive diagnosis. This case report presents a 61-year-old male patient with a single tumor in the right liver lobe, measuring approximately 101 mm × 99 mm. Initial imaging misdiagnosed the mass as hepatocellular carcinoma. Following multidisciplinary treatment discussions and subsequent tumor resection, histopathology and immunohistochemistry confirmed hepatic epithelioid angiomyolipoma. Accurate diagnosis of hepatic epithelioid angiomyolipoma is challenging, relying on histopathological examination and immunohistochemistry as diagnostic standards. Continuous monitoring of patients with hepatic epithelioid angiomyolipoma over an extended period is deemed essential. This report highlights the positive impact of multidisciplinary treatment in diagnosing and managing hepatic epithelioid angiomyolipoma.https://doi.org/10.1177/2050313X251314072
spellingShingle Da Teng
Yue Xu
Qingtao Meng
Qingsong Yang
Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review
SAGE Open Medical Case Reports
title Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review
title_full Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review
title_fullStr Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review
title_full_unstemmed Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review
title_short Unveiling the mystery of hepatic epithelioid angiomyolipoma: A unique case report with literature review
title_sort unveiling the mystery of hepatic epithelioid angiomyolipoma a unique case report with literature review
url https://doi.org/10.1177/2050313X251314072
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AT yuexu unveilingthemysteryofhepaticepithelioidangiomyolipomaauniquecasereportwithliteraturereview
AT qingtaomeng unveilingthemysteryofhepaticepithelioidangiomyolipomaauniquecasereportwithliteraturereview
AT qingsongyang unveilingthemysteryofhepaticepithelioidangiomyolipomaauniquecasereportwithliteraturereview