Pompe Disease: Early Diagnosis and Early Treatment Make a Difference

Pompe disease (glycogen storage disease type II or acid maltase deficiency) is a lysosomal disorder in which acid α-glucosidase (GAA) deficiencies lead to intralysosomal accumulation of glycogen in all tissues; most notably in skeletal muscles. Both the patient's age at the onset of Pompe disea...

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Bibliographic Details
Main Authors: Yin-Hsiu Chien, Wuh-Liang Hwu, Ni-Chung Lee
Format: Article
Language:English
Published: Elsevier 2013-08-01
Series:Pediatrics and Neonatology
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S1875957213000454
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