A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular Hyperplasia
Castleman's disease is a distinct form of lymph node hyperplasia divided into a solitary and a multicentric type. The solitary type occurs most commonly in the mediastinum and is usually asymptomatic. We present a patient with Castleman's disease of the hyaline-vascular solitary type locat...
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2013-01-01
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Series: | Case Reports in Surgery |
Online Access: | http://dx.doi.org/10.1155/2013/537593 |
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author | Theodosios Theodosopoulos Andreas Karakatsanis Anneza I. Yiallourou Fotios Nikolakopoulos Vassiliki Psychogiou Eleni Karvouni Dionysios Voros |
author_facet | Theodosios Theodosopoulos Andreas Karakatsanis Anneza I. Yiallourou Fotios Nikolakopoulos Vassiliki Psychogiou Eleni Karvouni Dionysios Voros |
author_sort | Theodosios Theodosopoulos |
collection | DOAJ |
description | Castleman's disease is a distinct form of lymph node hyperplasia divided into a solitary and a multicentric type. The solitary type occurs most commonly in the mediastinum and is usually asymptomatic. We present a patient with Castleman's disease of the hyaline-vascular solitary type located in the retroperitoneum.
The patient was a 38-year-old male, who presented to our hospital with fever. The imaging workup revealed a retroperitoneal mass, measuring 4 × 6 cm, located lateral to the aorta, inferior to the left renal artery and vein, and posterior to the left testicular vein. At workup, a solid hepatic lesion, 3 cm in diameter, located in the left lobe of the liver, segment IV, was also identified. Both lesions were surgically excised. The retroperitoneal tumor had the features of angiofollicular hyperplasia (Castleman's disease), hyaline-vascular type, whereas a diagnosis of focal nodular hyperplasia was made for the hepatic lesion. The patient is well at fourty months followup postoperatively. Surgical excision is the treatment of choice for unifocal Castleman's disease. |
format | Article |
id | doaj-art-08e11e96bf4b4616a79fdaa130cb3195 |
institution | Kabale University |
issn | 2090-6900 2090-6919 |
language | English |
publishDate | 2013-01-01 |
publisher | Wiley |
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series | Case Reports in Surgery |
spelling | doaj-art-08e11e96bf4b4616a79fdaa130cb31952025-02-03T01:02:04ZengWileyCase Reports in Surgery2090-69002090-69192013-01-01201310.1155/2013/537593537593A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular HyperplasiaTheodosios Theodosopoulos0Andreas Karakatsanis1Anneza I. Yiallourou2Fotios Nikolakopoulos3Vassiliki Psychogiou4Eleni Karvouni5Dionysios Voros62nd Department of Surgery, Aretaieion Hospital, University of Athens, 76 Vasilissis Sophias Avenue, 11528 Athens, Greece2nd Department of Surgery, Aretaieion Hospital, University of Athens, 76 Vasilissis Sophias Avenue, 11528 Athens, Greece2nd Department of Surgery, Aretaieion Hospital, University of Athens, 76 Vasilissis Sophias Avenue, 11528 Athens, Greece2nd Department of Surgery, Aretaieion Hospital, University of Athens, 76 Vasilissis Sophias Avenue, 11528 Athens, Greece2nd Department of Surgery, Aretaieion Hospital, University of Athens, 76 Vasilissis Sophias Avenue, 11528 Athens, GreeceDepartment of Pathology, Aretaieion Hospital, University of Athens, 76 Vasilissis Sophias Avenue, 11528 Athens, Greece2nd Department of Surgery, Aretaieion Hospital, University of Athens, 76 Vasilissis Sophias Avenue, 11528 Athens, GreeceCastleman's disease is a distinct form of lymph node hyperplasia divided into a solitary and a multicentric type. The solitary type occurs most commonly in the mediastinum and is usually asymptomatic. We present a patient with Castleman's disease of the hyaline-vascular solitary type located in the retroperitoneum. The patient was a 38-year-old male, who presented to our hospital with fever. The imaging workup revealed a retroperitoneal mass, measuring 4 × 6 cm, located lateral to the aorta, inferior to the left renal artery and vein, and posterior to the left testicular vein. At workup, a solid hepatic lesion, 3 cm in diameter, located in the left lobe of the liver, segment IV, was also identified. Both lesions were surgically excised. The retroperitoneal tumor had the features of angiofollicular hyperplasia (Castleman's disease), hyaline-vascular type, whereas a diagnosis of focal nodular hyperplasia was made for the hepatic lesion. The patient is well at fourty months followup postoperatively. Surgical excision is the treatment of choice for unifocal Castleman's disease.http://dx.doi.org/10.1155/2013/537593 |
spellingShingle | Theodosios Theodosopoulos Andreas Karakatsanis Anneza I. Yiallourou Fotios Nikolakopoulos Vassiliki Psychogiou Eleni Karvouni Dionysios Voros A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular Hyperplasia Case Reports in Surgery |
title | A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular Hyperplasia |
title_full | A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular Hyperplasia |
title_fullStr | A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular Hyperplasia |
title_full_unstemmed | A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular Hyperplasia |
title_short | A Rare Coexistence of Retroperitoneal Pararenal Castleman's Disease with Focal Nodular Hyperplasia |
title_sort | rare coexistence of retroperitoneal pararenal castleman s disease with focal nodular hyperplasia |
url | http://dx.doi.org/10.1155/2013/537593 |
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