Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver disease
Acquired hepatocerebral degeneration (AHD) and hepatolenticular degeneration can have similar clinical presentations, but when a chronic liver disease and atypical motor findings coexist, the distinction between AHD and hepatic encephalopathy (HE) can be even more complicated. We describe three case...
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| Format: | Article |
| Language: | English |
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Thieme Revinter Publicações
2011-06-01
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| Series: | Arquivos de Neuro-Psiquiatria |
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| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2011000400017&lng=en&tlng=en |
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| author | Fernando G. Romeiro Madileine F. Américo Fábio S. Yamashiro Carlos A. Caramori Arthur O. Schelp Antonio C. Santos Giovanni F. Silva |
| author_facet | Fernando G. Romeiro Madileine F. Américo Fábio S. Yamashiro Carlos A. Caramori Arthur O. Schelp Antonio C. Santos Giovanni F. Silva |
| author_sort | Fernando G. Romeiro |
| collection | DOAJ |
| description | Acquired hepatocerebral degeneration (AHD) and hepatolenticular degeneration can have similar clinical presentations, but when a chronic liver disease and atypical motor findings coexist, the distinction between AHD and hepatic encephalopathy (HE) can be even more complicated. We describe three cases of AHD (two having HE) with different neuroimaging findings, distinct hepatic diseases and similar motor presentations, all presenting chronic arterial hypertension and weight loss before the disease manifestations. The diagnosis and physiopathology are commented upon and compared with previous reports. In conclusion, there are many correlations among HE, hepatolenticular degeneration and AHD, but the overlapping of AHD and HE could be more common depending on the clinical knowledge and diagnostic criteria adopted for each condition. Since AHD is not considered a priority that affects the liver transplant list, the prognosis in AHD patients remains poor, and flow interruption in portosystemic shunts must always be taken into account. |
| format | Article |
| id | doaj-art-0782e6e7c4fa4e03bcb499a00db0820b |
| institution | OA Journals |
| issn | 1678-4227 |
| language | English |
| publishDate | 2011-06-01 |
| publisher | Thieme Revinter Publicações |
| record_format | Article |
| series | Arquivos de Neuro-Psiquiatria |
| spelling | doaj-art-0782e6e7c4fa4e03bcb499a00db0820b2025-08-20T02:02:50ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria1678-42272011-06-0169349650110.1590/S0004-282X2011000400017S0004-282X2011000400017Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver diseaseFernando G. Romeiro0Madileine F. Américo1Fábio S. Yamashiro2Carlos A. Caramori3Arthur O. Schelp4Antonio C. Santos5Giovanni F. Silva6Universidade Estadual PaulistaUniversidade Federal de Mato GrossoUniversidade Estadual PaulistaUniversidade Estadual PaulistaUniversidade Estadual PaulistaUniversidade de São PauloUniversidade Estadual PaulistaAcquired hepatocerebral degeneration (AHD) and hepatolenticular degeneration can have similar clinical presentations, but when a chronic liver disease and atypical motor findings coexist, the distinction between AHD and hepatic encephalopathy (HE) can be even more complicated. We describe three cases of AHD (two having HE) with different neuroimaging findings, distinct hepatic diseases and similar motor presentations, all presenting chronic arterial hypertension and weight loss before the disease manifestations. The diagnosis and physiopathology are commented upon and compared with previous reports. In conclusion, there are many correlations among HE, hepatolenticular degeneration and AHD, but the overlapping of AHD and HE could be more common depending on the clinical knowledge and diagnostic criteria adopted for each condition. Since AHD is not considered a priority that affects the liver transplant list, the prognosis in AHD patients remains poor, and flow interruption in portosystemic shunts must always be taken into account.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2011000400017&lng=en&tlng=enatetosecoréiadegeneração hepatolenticulardiscinesiasdistoniadistúrbios do movimentoencefalopatia hepáticahipercinesia |
| spellingShingle | Fernando G. Romeiro Madileine F. Américo Fábio S. Yamashiro Carlos A. Caramori Arthur O. Schelp Antonio C. Santos Giovanni F. Silva Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver disease Arquivos de Neuro-Psiquiatria atetose coréia degeneração hepatolenticular discinesias distonia distúrbios do movimento encefalopatia hepática hipercinesia |
| title | Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver disease |
| title_full | Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver disease |
| title_fullStr | Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver disease |
| title_full_unstemmed | Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver disease |
| title_short | Acquired hepatocerebral degeneration and hepatic encephalopathy: correlations and variety of clinical presentations in overt and subclinical liver disease |
| title_sort | acquired hepatocerebral degeneration and hepatic encephalopathy correlations and variety of clinical presentations in overt and subclinical liver disease |
| topic | atetose coréia degeneração hepatolenticular discinesias distonia distúrbios do movimento encefalopatia hepática hipercinesia |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2011000400017&lng=en&tlng=en |
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