Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature
Systemic cystic angiomatosis is a rare benign disorder due to the maldeveloped vascular and lymphatic system with less than 50 cases reported in literature so far. We report here a case of systemic cystic angiomatosis (SCA) with multisystem involvement affecting the neck, thyroid, thoracic cavity, a...
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| Format: | Article |
| Language: | English |
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Wiley
2017-01-01
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| Series: | Case Reports in Medicine |
| Online Access: | http://dx.doi.org/10.1155/2017/5032630 |
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| author | Vivek Kumar Trishala Meghal Yanyu Helen Sun Yiwu Huang |
| author_facet | Vivek Kumar Trishala Meghal Yanyu Helen Sun Yiwu Huang |
| author_sort | Vivek Kumar |
| collection | DOAJ |
| description | Systemic cystic angiomatosis is a rare benign disorder due to the maldeveloped vascular and lymphatic system with less than 50 cases reported in literature so far. We report here a case of systemic cystic angiomatosis (SCA) with multisystem involvement affecting the neck, thyroid, thoracic cavity, and skeletal system. The patient initially presented in her 4th decade of life with isolated lymphangioma in the neck requiring surgery. However, she experienced full-blown manifestations of SCA in her 6th decade which closely mimicked metastatic cancer. The diagnosis of SCA could only be established after multiple biopsies. The radiological and histological features of SCA with its course over 31 years in this patient have been described. |
| format | Article |
| id | doaj-art-06f09453e9d34b3abc9a5db4810e4a0a |
| institution | Kabale University |
| issn | 1687-9627 1687-9635 |
| language | English |
| publishDate | 2017-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Medicine |
| spelling | doaj-art-06f09453e9d34b3abc9a5db4810e4a0a2025-02-03T01:10:25ZengWileyCase Reports in Medicine1687-96271687-96352017-01-01201710.1155/2017/50326305032630Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the LiteratureVivek Kumar0Trishala Meghal1Yanyu Helen Sun2Yiwu Huang3Department of Internal Medicine, Maimonides Medical Center, Brooklyn, NY, USADepartment of Hematology and Oncology, Maimonides Cancer Center, Brooklyn, NY, USADepartment of Pathology, Maimonides Medical Center, Brooklyn, NY, USADepartment of Hematology and Oncology, Maimonides Cancer Center, Brooklyn, NY, USASystemic cystic angiomatosis is a rare benign disorder due to the maldeveloped vascular and lymphatic system with less than 50 cases reported in literature so far. We report here a case of systemic cystic angiomatosis (SCA) with multisystem involvement affecting the neck, thyroid, thoracic cavity, and skeletal system. The patient initially presented in her 4th decade of life with isolated lymphangioma in the neck requiring surgery. However, she experienced full-blown manifestations of SCA in her 6th decade which closely mimicked metastatic cancer. The diagnosis of SCA could only be established after multiple biopsies. The radiological and histological features of SCA with its course over 31 years in this patient have been described.http://dx.doi.org/10.1155/2017/5032630 |
| spellingShingle | Vivek Kumar Trishala Meghal Yanyu Helen Sun Yiwu Huang Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature Case Reports in Medicine |
| title | Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature |
| title_full | Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature |
| title_fullStr | Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature |
| title_full_unstemmed | Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature |
| title_short | Systemic Cystic Angiomatosis Mimicking Metastatic Cancer: A Case Report and Review of the Literature |
| title_sort | systemic cystic angiomatosis mimicking metastatic cancer a case report and review of the literature |
| url | http://dx.doi.org/10.1155/2017/5032630 |
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