Nonspecific therapy for Eisenmenger syndrome
Eisenmenger syndrome (ES) is systemic pulmonary hypertension with venoarterial or bidirectional shunting of blood between the ventricles, atria or great arteries due to the progression of pulmonary vascular disease in the natural course of “simple” and “complex” congenital heart defects.Patients wit...
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InterMedservice
2024-05-01
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| Series: | Евразийский Кардиологический Журнал |
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| Online Access: | https://www.heartj.asia/jour/article/view/6464 |
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| author | A. A. Shmalts I. E. Chernogrivov |
| author_facet | A. A. Shmalts I. E. Chernogrivov |
| author_sort | A. A. Shmalts |
| collection | DOAJ |
| description | Eisenmenger syndrome (ES) is systemic pulmonary hypertension with venoarterial or bidirectional shunting of blood between the ventricles, atria or great arteries due to the progression of pulmonary vascular disease in the natural course of “simple” and “complex” congenital heart defects.Patients with ES require constant attention from a multidisciplinary team of specialists. One of the main tasks is not to destabilize the fragile pathological physiology, which relies on the balance of pulmonary and peripheral vascular resistance. Surgical interventions with anesthesia, if they cannot be avoided, should be performed in specialized centers. Pregnancy is contraindicated in patients with ES. Clinical symptoms of blood hyperviscosity in ES are rare.The anachronistic practice of venesections, which leads to a decrease in the oxygen transport function of the blood, iron deficiency and an increased risk of cerebrovascular complications, should be avoided. Oral and intravenous replenishment of iron deficiency improves exercise tolerance and quality of life. Routine administration of anticoagulants for ES is not indicated. In most cases, endovascular embolization of pathological collateral arteries can eliminate hemoptysis. The use of venous access requires careful prevention of embolism. Therapeutic tactics for ES are discussed in detail in this review |
| format | Article |
| id | doaj-art-06acb9ac75ef47179d5761f30db0ba0a |
| institution | DOAJ |
| issn | 2225-1685 2305-0748 |
| language | Russian |
| publishDate | 2024-05-01 |
| publisher | InterMedservice |
| record_format | Article |
| series | Евразийский Кардиологический Журнал |
| spelling | doaj-art-06acb9ac75ef47179d5761f30db0ba0a2025-08-20T02:54:15ZrusInterMedserviceЕвразийский Кардиологический Журнал2225-16852305-07482024-05-010212213110.38109/2225-1685-2024-2-122-1316347Nonspecific therapy for Eisenmenger syndromeA. A. Shmalts0I. E. Chernogrivov1Bakoulev National Medical Research Center for Cardiovascular Surgery; Russian State Medical Postgraduate AcademyBakoulev National Medical Research Center for Cardiovascular SurgeryEisenmenger syndrome (ES) is systemic pulmonary hypertension with venoarterial or bidirectional shunting of blood between the ventricles, atria or great arteries due to the progression of pulmonary vascular disease in the natural course of “simple” and “complex” congenital heart defects.Patients with ES require constant attention from a multidisciplinary team of specialists. One of the main tasks is not to destabilize the fragile pathological physiology, which relies on the balance of pulmonary and peripheral vascular resistance. Surgical interventions with anesthesia, if they cannot be avoided, should be performed in specialized centers. Pregnancy is contraindicated in patients with ES. Clinical symptoms of blood hyperviscosity in ES are rare.The anachronistic practice of venesections, which leads to a decrease in the oxygen transport function of the blood, iron deficiency and an increased risk of cerebrovascular complications, should be avoided. Oral and intravenous replenishment of iron deficiency improves exercise tolerance and quality of life. Routine administration of anticoagulants for ES is not indicated. In most cases, endovascular embolization of pathological collateral arteries can eliminate hemoptysis. The use of venous access requires careful prevention of embolism. Therapeutic tactics for ES are discussed in detail in this reviewhttps://www.heartj.asia/jour/article/view/6464eisenmenger syndromecongenital heart defectstherapy |
| spellingShingle | A. A. Shmalts I. E. Chernogrivov Nonspecific therapy for Eisenmenger syndrome Евразийский Кардиологический Журнал eisenmenger syndrome congenital heart defects therapy |
| title | Nonspecific therapy for Eisenmenger syndrome |
| title_full | Nonspecific therapy for Eisenmenger syndrome |
| title_fullStr | Nonspecific therapy for Eisenmenger syndrome |
| title_full_unstemmed | Nonspecific therapy for Eisenmenger syndrome |
| title_short | Nonspecific therapy for Eisenmenger syndrome |
| title_sort | nonspecific therapy for eisenmenger syndrome |
| topic | eisenmenger syndrome congenital heart defects therapy |
| url | https://www.heartj.asia/jour/article/view/6464 |
| work_keys_str_mv | AT aashmalts nonspecifictherapyforeisenmengersyndrome AT iechernogrivov nonspecifictherapyforeisenmengersyndrome |