Neuronal ceroid-lipofuscinosis, a type of amaurotic family idiocy: clinical and pathological study of four cases

Neuronal ceroid-lipofuscinosis (NCL) is a recent term, proposed for acurate designation of the late-onset types of Amaurotic Family Idiocy (AFI). Histopathology shows ubiquitous intraneuronal accumulation of lipopigments, being the most important factor for characterization of the entity at present...

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Bibliographic Details
Main Authors: Luciano de Souza Queiroz, Joaquim N. da Cruz Neto, J. Lopes de Faria
Format: Article
Language:English
Published: Thieme Revinter Publicações 1974-03-01
Series:Arquivos de Neuro-Psiquiatria
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1974000100001&lng=en&tlng=en
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